产品编号：S692063
产品规格：5mg
产品价格：面议
| 标准品编号: | S692063 |
| 名称: | Succinylacetone-13C7 |
| 别名: | 4,6-Dioxoheptanoic Acid-13C7; NSC 174804-13C7; 4,6-Dioxoheptanoic-3,4,5,6,7-13C7 Acid; |
| CAS号: | 51568-18-4 |
| 参考CAS号: | Unlabelled: 51568-18-4 |
| 分子式: | ¹³C₇H₁₀O₄ |
| 外观: | Beige to Pale Brown Solid |
| 熔点: | 56-59°C |
| 分子量: | 165.1 |
| 储存: | -20°C Freezer, Under inert atmosphere |
| 溶解度: | DMSO (Slightly), Methanol (Slightly) |
| 类别: | Standards; Isotopic Labeled Analogues; Pharmaceutical/API Drug Impurities/Metabolites; |
| 应用: | Succinylacetone-13C7 is a labelled analogue of Succinylacetone (S692060). Succinylacetone (SA) is a specific marker for the inherited metabolic disease, hepatorenal tyrosinemia. It was developed a stable-isotope for the determination of SA in dried blood spots (DBS) and liquid urine using a 13C4-SA as internal standard. The method was applied retrospectively and prospectively for the diagnosis of hepatorenal tyrosinemia and for follow-up of patients under treatment. |
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