产品编号：I780753

产品规格：5mg

产品价格：面议

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产品详情

标准品编号:	I780753
名称:	N-Isobutyryl-d7-glycine
别名:	N-(2-methyl-1-oxopropyl-d7)glycine; N-Isobutyryl-d7-glycine;
CAS号:	1330037-23-4
参考CAS号:	15926-18-8 unlabelled
分子式:	C₆H₄D₇NO₃
分子量:	152.2
种类:	Building Blocks; Isotopic Labeled Analogues;
应用:	N-Isobutyryl-d7-glycine is labelled N-Isobutyrylglycine (I780750) which is a useful diagnostic tool in the diagnosis of many organic acidemias and mitochondrial fatty acid β-oxidation defects. N-Isobutyrylglycine detection is also used in the diagnosis of isobutyryl-CoA dehydrogenase deficiency.
参考文献	Costa, C. G. et al.: J. Pharmac. Biomed. Anal., 21, 1215 (2000); Bonafe, L. et al.: Mol. Gen. Metab., 69, 311 (2000); Sass, J. et al.: J. Inher. Metab. Dis., 27, 741 (2004);